Solid organ transplantation for non-TTR hereditary amyloidosis: report from the 1st International Workshop on the Hereditary Renal Amyloidoses Journal Article

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Authors: Stangou, A. J.; Lobato, L.; Zeldenrust, S.; Rela, M.; Portmann, B.; Linke, R. P.; Conceicao, I.; Otto, G.; Wilczek, H.; Suhr, O.; Azoulay, D.; Grateau, G.; Picken, M; O'Grady, J.; Heaton, N.; Ericzon, B. G.; Benson, M. D.
Article Title: Solid organ transplantation for non-TTR hereditary amyloidosis: report from the 1st International Workshop on the Hereditary Renal Amyloidoses
Abstract: Fibrinogen A alpha-chain (AFib) and apolipoprotein AI (AApoAI) amyloidosis due to variants in the AFib and ApoAI genes are the most common types of hereditary amyloidosis in Europe and the United States. Liver is the exclusive source of the aberrant amyloidogenic protein in AFib and responsible for supplying approximately half of the circulating variant ApoAI. Nephrotic syndrome and renal impairment due to renal amyloidosis are common disease manifestations; however, recent research provides evidence to support a more diverse and systemic disease phenotype, which in turn has implications in the management of the hereditary amyloidoses with solid organ transplantation and, in particular, liver transplantation.
Journal Title: Amyloid : the international journal of experimental and clinical investigation : the official journal of the International Society of Amyloidosis
Volume: 19 Suppl 1
ISSN: 1744-2818; 1350-6129
Publisher: Unknown  
Journal Place: England
Date Published: 2012
Start Page: 81
End Page: 84
Language: eng
DOI/URL:

10.3109/13506129.2012.668503
Notes: ID: 12349; JID: 9433802; 2012/04/27 [aheadofprint]; ppublish
LUC Authors
  1. Maria M. Picken
    74 Picken
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